Muammer Melih ŞAHİN, Mehmet DÜZLÜ, İpek Işık GÖNÜL, Arzu OKUR, Raşit CEVİZCİ, Faruk Güçlü PINARLI, İbrahim Onur ÖZEN, Recep KARAMERT, Metin YILMAZ, Utku AYDİL

An Atypical Presentation of Renal Cell Carcinoma in a Child: A Neck Mass

Adölesan dönemde baş boyun bölgesinde en sık rastlanılan malign hastalıklar; akut lösemi, Hodgkin lenfoma, non-Hodgkin lenfoma, nazofarenks kanseri ve tiroid kanseridir. Renal hücreli karsinom (RHK) servikal lenf nodlarına metastaz yapabilmekle beraber, çocukluk döneminde görülmesi ve boyun kitlesi ile başvurusu çok nadirdir. Bu yazıda ilk başvuru şikayeti sol boyunda kitle olan on altı yaşında bir kız çocuğunu sunuyoruz. Hastanın sol böbreğinde yerleşik olduğu tespit edilen primer tümör ve boyun metastazı eksize edildi ve patolojik tanı translokasyonal renal hücreli karsinom olarak rapor edildi. Abdominal ve torasik malignensiler metastatik lenf nodları ile prezente olabileceğinden çocuklarda boyun kitlelerine yaklaşımda ayırıcı tanıda bulundurulmalıdır

Atipik Prezentasyonlu Bir Pediatrik Renal Hücreli Karsinom Vakası: Boyunda Kitle

The most common malignant diseases of the head and neck in the adolescent period are acute leukemia, Hodgkin's disease, non-Hodgkin's lymphoma, nasopharyngeal carcinoma, and thyroid carcinoma. Although renal cell carcinoma (RCC) may metastasize in the cervical lymph nodes, both occurrence and presentation as a neck mass are rare in the childhood period. In this report, we present a sixteen-year-old girl who was admitted with a left neck mass at presentation. The primary tumor was found to be located in the left kidney and both masses were surgically removed, revealing a diagnosis of a translocation renal cell carcinoma with metastases. Distant metastases of abdominal and thoracic malignancies may present with metastatic lymph nodes, and should be included in the differential diagnosis of the neck masses in children

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