Fatih Köksal BİNNETOĞLU, Naci TOPALOĞLU, Mustafa TEKIN, Şule YIDIRIM, Nazan KAYMAZ, Abdullah SARIYILDIRIM

Nadir Bir Birliktelik; Pulmoner Arter Sling ve Mowat Wilson Sendromu

Sol pulmoner arterin sağ pulmoner arterden çıktığı pulmoner sling anomalisi nadir bir vaskülerhalka tipi olup trakeaya ve özafagusa bası yaparak solunum sıkıntısı, öksürük, hırıltı, stridor,beslenme problemleri ve tekrarlayan kusmalara yol açabilir. Bu yazıda dismorfik yüz yapısı,hafif mental retardasyon nedeniyle izlenen ve üfürüm nedeniyle yapılan ekokardiyografidepulmoner arter sling anomalisi saptanan 14 yaşındaki bir olgu sunulmuştur

Anahtar Kelimeler:

Mowat Wilson Sendromu, pulmoner arter sling, vasküler halka

A Rare Association; Pulmonary Artery Sling and Mowat-Wilson Syndrome

Pulmonary artery sling anomaly, where the left pulmonary artery originates from the rightpulmonary artery is a rare type of vascular ring that can cause respiratory difficulties, cough,wheezing, stridor, feeding difficulties and repetitive vomiting due to tracheal and esophagealcompression. We present a 14-year-old patient with dysmorphic facial appearance and mildmental retardation who underwent an echocardiography for murmur and was diagnosed withpulmonary artery sling anomaly

Keywords:

Mowat Wilson syndrome, pulmonary artery sling, vascular ring,

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