Hakan UZUN, Ahmet HAZNEDAROGLU, Nese ERSÖZYAR, Dursun Ali SENSES, Kenan KOCABAY

Bir Primer Lenfödem Olgusu

Lenfödem, sivi, makromolekül ve hücreler içeren asiri kapiller filtratin kana geri geçisinde lenfatik sistemde bir yetmezlik olmasindan kaynaklanan ödem ya da doku sisligidir. Genellikle, Flariaz, cerrahi travma ya da enfeksiyon gibi durumlara ikincil olarak gelisir. Primer lenfödemde bir genetik yatkinlik oldugu düsünülmektedir. Sporadik veya kalitsal olabilir; lenfatik sistemin gelisimi veya islevinde bir sorundan kaynaklanmaktadir. Bu çalismada, bir alt ekstremitesinde primer lenfödem gelisimi olan on iki yasindaki bir kiz hasta sunulmaktadir. Lenfödem patogenezi ve siniflandirmasi kisaca gözden geçirilmektedir

Anahtar Kelimeler:

Primer lenfödem siniflamasi, çocuk

A Case of Primary Lymphedema

Lymphedema is edema or tissue swelling resulting from failure of the lymphatic system to transport excess capillary filtrate containing liquid, macromolecules, and mobile cells back to the blood. It is usually secondary to filariasis, surgery, trauma, or infection. Primary lymphedema is thought to have a strong genetic component and arises from faulty development or function of the lymphatic system. It can be sporadic or inherited. In study a case of primary lymphedema in the left lower extremity in a 12 years old girl was presented. Pathogenesis and classification of primary lymphedema were briefly reviewed

Keywords:

Primary lymphedema classification, child,

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