Erdal BODAKÇİ, Mazhar Müslüm TUNA, FARUK KILINÇ, ZAFER PEKKOLAY, Hikmet SOYLU, ŞADİYE ALTUN TUZCU, Alpaslan Kemal TUZCU

A rare cause of acromegaly: McCune-Albright syndrome

McCune-Albright sendromu, poliostotik fibröz displazi, deride kahverenginde lekelenme (Cafe au lait lekeleri) ve otonomik endokrin hiperfonksiyon ile karakterize bir sendromdur. Bu sendromda yaygın olarak erken puberte ve diğer endokrinolojik manifestasyonlar örneğin akromegali, jigantizm, hiperkortizolizm görülebilir. Akromegali Mc-Cune-Albriht sendromlu hastaların % 20 sinde görülebilir. Biz bu sendroma eşlik eden bir akromegali vakasını sunduk

Akromegalinin nadir bir nedeni: McCune-Albright sendromu

McCune-Albright syndrome is characterized by polyostat- ic fibrous dysplasia, brown spots on the skin (café au lait pigmentation) and autonomous endocrine hyperfunction. Early puberty and other endocrinological manifestations, such as acromegaly, gigantism and hypercortisolism are widely observed in the syndrome. Acromegaly is seen in 20% of patients. We report a case of acromegaly accom- panied with this syndrome.

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