ŞEBNEM KADER, Pınar Gökçe REİS, MEHMET MUTLU, Yakup ASLAN, EROL ERDURAN, UĞUR YAZAR

A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report

İntrakranial kanamalar term yenidoğanlarda nadir görülen, morbidite ve mortalitesi yüksek bir klinik tablodur. Majör kanamalar nispeten nadir olmasına rağmen, hemofilik çocuklarda yaşamın ilk birkaç gününde doğum travmasına bağlı gelişebilecek intrakranial kanama insidansı, çocukluğun herhangi bir evresine göre daha yüksektir. Burada, ailesinde hemofili öyküsü bulunmayan, intrakranial ve ekstrakranial hemoraji ile başvurup orta derecede hemofili A tanısı konan bir yenidoğan olgusunu sunmayı ve erken teşhis ve replasman tedavisinin hayati bir öneme sahip olduğunu vurgulamayı amaçladık.

Ağır intrakranial ve ekstrakranial kanaması olan orta hemofili A tanılı bir yenidoğan: Olgu sunumu

Intracranial hemorrhage among term newborns is a rare clinical condition with high morbidity and mortality. Although major bleeding is relatively uncommon, the incidence of intracranial hemorrhage in hemophilic children is higher during the first few days of life than at any other stage in childhood, which relates to the trauma of delivery. Here, we reported a newborn case diagnosed with moderate hemophilia A, without the presence of a positive family history of hemophilia and presenting with intracranial and extracranial hemorrhage and we aimed to emphasize that the early diagnosis and replacement therapy carries an essential importance.

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