Hande KURTULGAN KÜÇÜK, Şenol ÇİTLİ, Gülseren GÖKTOLGA ERKOCA, İlhan SEZGİN

VATER asosiasyonu: Bir olgu sunumu

VATER asosiasyonu (V: Vertebral anomali, VSD ve diğer kardiyak defektler; A: Anal atrezi veyafistül; T-E: Trakeaözefagial fistül ile özefagus atrezisi; R: Radial displazi, başparmak veya radialhipoplazi, preaksial polidaktili, sindaktili, renal anomali) çeşitli anomaliler ile karekterize olan birkonjenital bozukluktur. Sunulan olguda opere özefagus atrezisi ve trakeaözefagial fistül, operevestibuler anüs ve anal atrezi, sol el başparmak yokluğu, sol el 5.parmakta klinodaktili, pektuscarinatus, skolyoz, dolikosefali, kısa boyun, basık ve geniş burun kökü, kepçe kulak, sakral dimplebulunan 4 yaşında bir kız çocuğu tanımlanmıştır.

VATER accosiation: A case report

VATER association, (V: Vertebral anomaly, VSD and other cardiac defects; A: Anal atresia orfistula; T-E: Tracheoesophageal fistula with esofageal atresia; R: Radial dysplasia, thumb or radialhypoplasia, preaxial polidactyly, syndactyly, renal anomaly) is a relatively rare pattern of multiplecongenital abnormalities. İn this case, a 4-year-old female child with tracheoesophageal fistulawith esophageal atresia, vestibuler anus and anal atresia, left thumb agenesis and clinodactyly inleft hand fifth finger, pectus carinatus, scoliosis, short neck, broad and depressed nose, prominentear and sacral dimple is described.

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