Promil JAIN, Sunita SINGH, K N RATTAN, Narinder DAHIYA, Sneh SINGH, S K MATHUR

Askin Tumour: A rare childhood thoraco - pulmonary malignancy of Ewing's family of umours

Göğüs duvarının primitif nöro-ektodermal tümörü veya diğer bir deyişle Askin tümörü nadirgörülen bir küçük hücreli nöroepitelyoma olup göğüs duvarı veya akciğer kökenlidir. Ağırlıklıolarak çocuk ve adolesanlarda saptanır. Her ne kadar ışık mikroskopisindeki görünümü Ewingsarkomu, rabdomyosarkom, nöroblastom ve lenfoma gibi bu yaş grubunda çoğunlukla görülengöğüs duvarı neoplasmlarına benzese de Askin tümörü farklı bir antitedir. Bu makalede yüksekderecede agresif klinik seyirli, torakopulmoner alan yerleşimli nadir bir malignite olan Askintümörlü bir çocuk hasta sunulmuştur.

Askin Tümörü: Ewing tümör ailesinin nadir görülen çocukluk çağı torakop ulmoner malignitesi

Primitive neuro-ectodermal tumour of chest wall or the Askin tumour is a rare, malignant smallcell neuroepithelioma that arises from the chest wall or lung. It is seen predominantly in childrenand adolescents. Although its appearance by light microscopy is similar to Ewing s sarcoma,rhabdomyosarcoma, neuroblastoma and lymphoma, which account for bulk of chest wallneoplasms in this age group, yet the Askin tumour is a distinct entity. We present a case of Askintumour in a child, a rare malignant tumour in the thoraco-pulmonary area with highly aggressiveclinical course.

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