İdiyopatik ana pulmoner arter anevrizma onarımı

İdiyopatik ana pulmoner arter anevrizması patogenezi tam olarak anlaşılamamış, nadir görülen bir durumdur. Kırküç yaşında kadın hasta 6 cm çapında dev ana pulmoner arter anevrizması tanısıyla kliniğimize yatırıldı. Etyolojide altta yatan bir hastalık bulunamadı, idiyopatik olduğu kabul edildi. Ameliyatta mediyan sternotomi yapıldı, kardiyopulmoner bypassa girildi. Ana pulmoner arter longitudinal olarak açıldı. Pulmoner arter duvar kalınlığı ve yapısı normal görünümdeydi. Anevrizmanın ön yüzünden yaklaşık 5 cm uzunluğunda 2.5 cm genişliğinde eliptik bir kısım çıkarılarak redüksiyon arteriyoplasti yöntemiyle pulmoner arter daraltıldı. Hasta sorunsuz taburcu edildi.

Surgical treatment of idiopathic main pulmonary artery aneurysm

Idiopathic pulmonary artery aneurysms are rare anomalies with poorly understood pathogenesis. A 43-year-old female patient with a giant main pulmonary artery aneurysm of 6 cm in diameter was referred to our institution. The etiology of the aneurysm could not be identified, therefore it was accepted as idiopathic. After median sternotomy cardiopulmonary bypass was instituted. The pulmonary artery was opened longitudinally. The wall thickness and structure of the pulmonary artery was normal. An eliptic shaped part of the anterior wall of the aneurysm of 5x2.5 cm in dimensions was resected and the pulmonary artery narrowed. After the reduction arterioplasty the patient was discharged without complications.

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