Evren ÜSTÜNER, Deniz TUNCEL, Nursel AYDIN, İlhan ERDEN, Ayşe ERDEN

Olgu sunumu: Amyotrofik lateral sklerozda kranial MRG bulguları

49 yaşında disfaji ve disartri bulguları ile başvuran amyotrofik lateral sklerozlu (ALS) bir erkek hastayı sunuyoruz. Fizik muayenesinde tüm derin tendon refleksleri artmıştı ve distal üst ekstremitede kas atrofisi ile birlikte, patolojik refleksler izlenmekteydi. MR görüntüleme, T2 ağırlıklı görüntülerde medulla oblangatadan subkortikal presantral gyrusa dek kortikospinal traktta simetrik ve bilateral artmış sinyal intensitesini gösterdi. T1 ağırlıklı görüntülerde kapsula internanın arka bacağında artmış sinyal intensitesi izlendi. MR görüntüleme ALS'yi taklit eden patolojileri dışlamada yararlıdır ve ALS hastalarının tanı ve takibinde potansiyel role sahiptir.

Case report: Cranial MRI findings in Amytrophic lateral sclerosis

We describe a 49-year-old man with amyotrophic lateral sclerosis (ALS) who presented with dysphagia and dysarthria. Deep tendon reflexes in the limbs were increased and pathological reflexes were recorded along with muscular atrophy of the distal upper extremities. MR imaging revealed symmetric and bilateral increased signal intensity on T2-weighted images in the corticospinal tract from medulla oblangata to subcortical precentral gyrus. Increased signal intensity at the posterior limb of capsula interna on T1-weighted images were also detected. MR imaging is beneficial in ruling out pathologies that may mimic ALS, and may have potential role in the diagnosis and follow up of ALS patients.

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