Aysun YILMAZLAR, Bahittin NAZLI, Hüseyin OĞUZALP

Crouzon sendromunda hava yolu yönetimi

Crouzon sendromu kranyosinostoz. hipertelorizm, orbital proptozis. küçük üst dudak, hipoplastik maksilla, relatif mandibuler prognotizm ve ekstremi t e gelişiminde gerilik ile karakter ize otozomal dominant geçen bir sendromdur. Kranyosinostozu, anormal kranium gelişimi, artmış kafa içi basıncı, rölatif mandibular prognotismi ve ekstremite gelişiminde geriliği olan Crouzon sendromlu bir olguyu sunduk. Bu sendronıda ventrikülo-peritoneal şant yerleştirilmesi ameliyatında anestezi yönetimi ve hava yolu yönetiminde dikkat edilmesi gereken noktaları vurgulamak istedik.

Airway management in crouzon syndrome

Crouzon syndrome is an autosomal dominant disorders in patients with craniosynostosis, hypertelorism, orbital proptosis, short upper lip, hypoplastic maxilla, relative prognathism and without extremity involvement. We presented anaesthetic management of a Crouzon syndrome with craniosynostosis, abnormal cranial involvement, increased intracranial pressure, relative prognathism and without extremity involvement who undergoes ventriculo-peritoneal shunt operation. We wanted to emphasize the points which should be considered for patients with in providing anesthesia and airway patency in this syndrome.

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