Karamehmet YILDIZ, Halit MADENOĞLU, Kudret DOĞRU, Adem BOYACI

Apert sendromu ve anestezi (Olgu sunumu)

Apert Sendromu kranyosinostoz, maksillar hipoplazi ve sindaktili ile karakterize kongenital bir hastalıktır. Bu olgu sunumunda, aynı zamanda literatürde yer alan olguların en küçüğü olan (50 günlük), Apert sendromlu olgumuza uyguladığımız genel anestezi yönteminin tartışılması ve konu ile ilgili literatür bilgilerinin gözden geçirilmesi amaçlanmıştır.

Anahtar Kelimeler:

Kraniyofasiyal anomaliler, Akrosefalosindaktili, Anestezi, genel

Apert syndrome and anesthesia (Case report)

Apert Syndrome is a congenital illness characterised by craniosynostosis, maxillary hypoplasia and syndactyly. In our case presentation, we aimed to discuss the anesthetic method we applied to the patient with Apert syndrome, which was youngest case in the literature and to look over the literature knowledge related with this matter.

Keywords:

Craniofacial Abnormalities, Acrocephalosyndactylia, Anesthesia, General,

PDF

___

1. Vijayalakshmi AM, Menon A. Apert Syndrome. Indian Pediatrics 2002;39:876-8.
2. Elwood T, Sarathy PV, Geiduschek JM, Ulma GA, Karl HW. Respiratory complications during anesthesia in Apert syndrome. Paed Anaesth 2001;11:701-3.
3. McGill T. Otolaryngologic aspects of Apert syndrome. Clin Plast Surg 1991;18:309-13.
4. Moore MH. Upper airway obstruction in the syndromal craniosynostoses. Br J Plast Surg 1993;46:355-62.
5. Morris GP, Cooper MG. Difficult tracheal intubation following midface distraction surgery. Paed Anaesth 2000; 10:99-102.
6. Mixter RC, David DJ, Perloff WH, Green CG, Pauli RM. Obstructive sleep apnea in Apert's and Pfeiffer's syndromes: More than a craniofacial abnormality. Plast Reconstruct Surg 1990;86:457-63.
7. Nargozian C. Apert syndrome: Anesthetic management. Clin Plast Surg 1991; 18:227-30.
8. Rolf N, Cote CJ. Frequency and severity of desaturation events during general anesthesia in children with and without upper respiratory infections. J Clin Anesth 1992;4:200-3.
9. Sloan M, Conard P, Karsunky P, et al. Sevoflurane versus izoflurane: Induction and recovery characteristics with single-breath inhaled inductions of anesthesia. Anesth Analg 1996;82;528-32.
10. Doi M, Ikeda K. Airway irritation produced by volatile anaesthetic during brief inhalation: comparison of halothane, enflurane, isoflurane and sevoflurane. Can J Anaesth 1993;40:122-6.