Bahar MÜEZZİNOĞLU, Sibel KILIÇALP, Gülçin BAŞDEMİR, Fikri ÖZTOP

Fibroz Displazi ve Anevrizmal Kemik Kisti Birlikteliği

Fibroz displazi iskelet gelişimini etkileyebilen benign fibroosseöz bir lezyondur. Tipik histolojik görüntüsü yanında kistik gelişim alanları, kanama, kıkırdak dokusu varlığı FD’ye eşlik edebilir. Anevrizmal kemik kisti ise kemiğin nonneoplastik, şişirgen bir lezyonudur. Primer olarak izlenebileceği gibi sıklıkla malign veya benign kemik lezyonlarıyla da beraberlik gösterebilir. Ege Üniversitesi Tıp Fakültesi Patoloji Anabilim Dalı’nda tanı alan 71 fibroz displazi olgusunda anevrizmal kemik kisti alanlarının varlığı araştırıldı. Anevrizmal kemik kisti alanları içeren 7 olgu saptandı. Bu olguların yaş, cinsiyet ve yerleşim yerine göre dağılımları incelendiğinde genç yaşta (ortalama 22,6) görüldüğü, tümünün uzun kemiklerde yerleştiği (6 femur, 1 tibia) ve kadınlarda erkeklerden daha fazla olduğu (5 kadın, 2 erkek) görüldü.

Anahtar Kelimeler:

Fibroz displazi, anevrizmal kemik kisti

Fibrous Dysplasia Associated With Aneurysmal Bone Cyst

Fibrous dysplasia is a benign pathologic condition that affects skeletal maturation. Besides its typical hystopathologic morphology cysts, hemorrhage, chondromatous areas may accompany fibrous dysplasia. Aneurysmal bone cyst is a nonneoplastic expansile bone lesion. It can exist either as a primary bone lesion or as a secondary lesion arising in other benign or malignant osseous conditions. Seventy one cases diagnosed as fibrous dysplasia in Ege University Pathology Department were reviewed in order to reveal any association with aneurysmal bone cyst. In seven cases microscopic changes of aneurysmal bone cyst were identified. Age ,sex and site distribution were as follows: young age (mean age of 22.6), all localised to long bones (6 femur, 1 tibia) with female preponderance (5 females, 2 males).

Keywords:

Fibrous dysplasia, aneurysmal bone cyst,

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