Oğuz Kaan ÜNAL, Osman Serhat GÜNER, Mehmet MERİÇ

Post-Partum Dönemde Menstrüasyon ile Tetiklenen Ailevi Akdeniz Ateşi Olgusu

Ailevi Akdeniz Ateşi FMF , periyodik olarak ortaya çıkan ateş, karın ağrısı, poliserözit ve erezipel benzeri döküntülerle karakterize herediter geçişli bir hastalıktır. Akdeniz ve yakın Ortadoğu bölgesinden adını alan hastalık Türk, Ermeni, Yahudi ve Araplar gibi bazı etnik gruplara spesifiktir. FMF genetik geçişli otozomal resesif bir hastalıktır. 32 yaşında bayan hasta ilk doğum sonrası menstrüasyon başlamasıyla periyodik olarak ortaya çıkan şiddetli karın ağrısı şikayeti ile başvurdu. Karın ağrısına ateş yüksekliği, döküntü ya da artrit gibi ek semptomlar eşlik etmiyordu. Pozitif aile öyküsü bulunması nedeni ile tetkik edilen hastaya FMF tanısı kondu. Menstrüasyon dönemlerinde siklik olarak kolşisin tedavisi düzenlenerek atakları kontrol altına alındı

Familial Mediterranean Fever Which Was Induced Menstruat Ion At Post-Partum Period

Familial Mediterranean fever FMF is a hereditary disease characterised by recurrent attacks of fever with peritonitis, pleuritis, arthritis or erysipelas-like rash. As its name suggests, FMF is seen primarily among individuals of Mediterranean ancestry, particularly Turks, Armenians, non-Ashkenazi Jews and Arabs. Familial Mediterranean fever is inherited as an autosomal recessive disorder. 32 year old female patient was admitted with severe abdominal pain occurring periodically with the onset of first menstruation after pregnancy. Abdominal pain was not accompanied by additional symptoms such as fever, rash or arthritis. The patient who is investigated due to positive family history was diagnosed with FMF. Episodes were controlled by cyclic colchicine treatment which was given at the perimenstrual period

Keywords:

Familial Mediterranean Fever, menstruation, pregnancy,

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