Yurda ŞİMŞEK, Gamze GEZGEN, Özge YILMAZ, Hasan YÜKSEL

Komplikasyonlari ile VACTERL Asosiasyonu

VACTERL asosiasyonu; vertebral, anorektal, kardiyak, trakeoözafagial, renal ve ekstremite anomalilerinden en az üç tanesinin birarada olduğu 1/10000-1/40000 sıklıkta saptanan bir klinik durumdur. Spesifik bir etiyoloji tanımlanmamıştır ve tanı klinik bulgulara dayanır. Bu makalede, VACTERL asosiyasyonu gözden geçirilmiş ve yineleyen trakeoözofagial fistül ve havayolu hiperreaktivitesi olan 18 aylık erkek olgunun sunumu ile klinik bulgular ve komplikasyonların izlemi vurgulanmıştır.

Anahtar Kelimeler:

Trakeoözafagial fistül, VACTERL asosiyasyonu

VACTERL Association and Its Complications

VACTERL association is a clinical condition, detected at a frequency of 1/10000-1/40000, in which at least three of vertebral, anorectal, cardiac, tracheoesophageal, renal and extremity anomalies coexist. No specifi c etiology has been described and the diagnosis is based upon clinical fi ndings. In this article, the VACTERL association was reviewed and follow up of clinical fi ndings and complications were presented by reporting an 18-month-old male with recurrence of tracheoesophageal fi stula and hyperreactive airway disease

Keywords:

Tracheoesophageal fi stula, VACTERL association,

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