Özge YILMAZ, Hasan YÜKSEL, Yurda ŞİMŞEK, Gamze GEZGEN

Komplikasyonları ile VACTERL Asosiasyonu

VACTERL asosiasyonu; vertebral, anorektal, kardiyak, trakeoözafagial, renal ve ekstremite anomalilerinden en az üçtanesinin birarada olduğu 1/10000-1/40000 sıklıkta saptanan bir klinik durumdur. Spesifik bir etiyoloji tanımlanmamıştır vetanı klinik bulgulara dayanır. Bu makalede, VACTERL asosiyasyonu gözden geçirilmiş ve yineleyen trakeoözofagial fistül vehavayolu hiperreaktivitesi olan 18 aylık erkek olgunun sunumu ile klinik bulgular ve komplikasyonların izlemi vurgulanmıştır.

VACTERL Association and Its Complications

VACTERL association is a clinical condition, detected at a frequency of 1/10000-1/40000, in which at least three ofvertebral, anorectal, cardiac, tracheoesophageal, renal and extremity anomalies coexist. No specific etiology has beendescribed and the diagnosis is based upon clinical findings. In this article, the VACTERL association was reviewed andfollow up of clinical findings and complications were presented by reporting an 18-month-old male with recurrence oftracheoesophageal fistula and hyperreactive airway disease.

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