Gökhan ARSLAN, Fırat KARDELEN, Gayaz AKÇURİN, Abdullah KOCABAŞ, Halit ERTUĞ

Çıkan Aortadan Anormal Kaynaklanan Sağ Pulmoner Arter, Aortopulmoner Pencere ve Kesintili Arkus Aorta Birlikteliği: Tek 3d Yama ile Başarılı Cerrahi Düzeltme

Çıkan aortadan anormal kaynaklanan sağ pulmoner arter (ÇAAKPA) nadir görülen bir konjenital kalp defekti olup genellikle başka kalp anomalilerine eşlik eder. ÇAAKPA’lı hastalarda artmış pulmoner kan akımı sonucunda konjestif kalp yetmezliği ve tek taraflı pulmoner hipertansiyon gelişir. Bu nedenle cerrahi düzeltme yapılmayan hastalar genellikle yenidoğan ya da erken süt çocukluğu döneminde hayatını kaybederler. Bu yazıda, ÇAAKPA, aortopulmoner pencere ve kesintili arkus aorta birlikteliği saptanan ve tek 3D ksenograft yama kullanılarak başarılı bir şekilde opere edilen 1.5 aylık kız hasta sunulmaktadır.

Anahtar Kelimeler:

Çıkan aortadan anormal kaynaklanan sağ pulmoner arter, Aortopulmoner pencere, Konjenital kalp hastalığı, Kesintili arkus aorta

Anomalous Origin of the Right Pulmonary Artery from Ascending nomalous Origin of the Right Pulmonary Artery from Ascending Aorta Associated with Aortopulmonary Window and Interrupted orta Associated with Aortopulmonary Window and Interrupted Aortic Arch: Successful Surgical Correction with

Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA) is a rare congenital heart defect and generally associated with other cardiac anomalies. Patients with AORPA have high pulmonary fl ow results in congestive heart failure and unilateral pulmonary hypertension. Thus, it is frequently a fatal malformation in the neonatal or early infancy periods if early surgical repair is not performed. Herein, we report a 1.5 month-old girl who was diagnosed with AORPA associated with aortopulmonary window and interrupted aortic arch and successfully operated using a single pericardial xenograft 3D patch

Keywords:

Anomalous origin of the right pulmonary artery from ascending aorta, Aortopulmonary window, Congenital heart defect, Interrupted aortic arch,

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