Yeliz ÇAĞAN APPAK, Erhun KASIRGA, Güzide DOĞAN, Serdar TARHAN

Abernethy Malformasyonu: Konjenital Ekstrahepatik Portokaval Şantın Nadir Nedeni

Abernethy malformasyonu birçok farklı klinik bulgu ile görülebilen çok nadir bir splanknik venöz sistem anomalisidir. Bu olgu sunumunda klinik bulgusu olmadan tetkikler sonucunda rastlantısal olarak Abernethy malformasyonu saptanan ve karaciğerde kitleleri bulunan 5 aylık kız olgu sunulmaktadır. Malformasyonun klinik bulguları ve olası komplikasyonların önemi vurgulanmaktadır.

Anahtar Kelimeler:

Çocuk, Portal ven, Vasküler malformasyon

The Abernethy Malformation: A Rare Cause of Congenital Extrahepatic Portacaval Shunt

The Abernethy malformation is a rare anomaly of the splanchnic venous system with a widely variable clinical presentation. In this case report we presented a 5-month-old girl where liver masses and the Abernethy malformation were incidentally detected without clinical symptoms as a result of investigations. Clinical fi ndings of the malformation and the importance of potential complications are emphasized

Keywords:

Child, Portal vein, Vasculer malformation,

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