Regional odontodisplasia is a developmental anomaly of dental tissues with characteristic clinical, radiographic and histologic appearances. It most commonly affects the maxillary anterior teeth of both the primary and permanent dentition, and occurs in females twice as often as in males. The pathogenesis is unknown. A case of a twelve- year old female with regional odontodisplasia is presented. Although the affected teeth displayed the radiographical and clinical features of odontodisplasia, the patient appeared with significant soft tissue swelling on the anterior region of the mandible.

Regional odontodisplasia is a developmental anomaly of dental tissues with characteristic clinical, radiographic and histologic appearances. It most commonly affects the maxillary anterior teeth of both the primary and permanent dentition, and occurs in females twice as often as in males. The pathogenesis is unknown. A case of a twelve- year old female with regional odontodisplasia is presented. Although the affected teeth displayed the radiographical and clinical features of odontodisplasia, the patient appeared with significant soft tissue swelling on the anterior region of the mandible.