Mehmet BALKANAY, Erhan KAYA, Mehmet Erdem TOKER, Cevat YAKUT, Ercan EREN, Mustafa GÜLER

Type II aortopulmonary window coexisting with a ventricular septal defect in a 23-year-old man

Aortopulmoner pencere nadir bir doğumsal kardiyak anomalisidir. Yirmi-üç yaşındaki bir erkek hastada aortopulmoner pencere ve buna eşlik eden ventriküler septal defekt saptandı. Hastanın öyküsünden, yedi yaşında iken sistolik üfürüm saptandığı ve o tarihten itibaren sadece medikal tedavi ile izlendiği öğrenildi. İkiboyutlu ve Doppler ekokardiyografik incelemede tip II aortopulmoner pencere ve ventriküler septal defekt görüldü. Tanı kardiyak kateterizasyon ve anjiyografi ile doğrulandı. Hastaya transaortik yaklaşımla cerrahi düzeltme uygulandı. On altı aylık izlem sonunda hastanın durumu New York Heart Association sınıf I'e uymaktaydı.

Yirmi üç yaşındaki erkek olguda tip II aortopulmoner pencere ile birlikte ventriküler septal defect

Aortopulmonary window is a rare congenital cardiac anomaly. We herein report a case of an aortopulmonary window coexisting with a ventricular septal defect in a 23-year-old man. He had a history of a systolic murmur detected when he had been seven years old, after which he had been followed-up only with medications. Two-dimensional and Doppler echocardiography showed a type II aortopulmonary window and an inlet type ventricular septal defect. The diagnosis was confirmed by cardiac catheterization and angiography. Surgical correction was performed using the transaortic approach. After a follow-up of 16 months, the patient was in New York Heart Association class I.

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