Levent SALTIK, Erhan KANSIZ, Gürkan ÇETİN, Ahmet ÖZKARA, ÖZge KÖNER

Transposition of the great arteries with ventricular septal defect and interrupted aortic arch: A successfull surgical correction with one stage and two separate incisions

Büyük arterlerin transpozisyonu ile birlikte ventriküler septal defekt ve aorta kavsinin interapsiyonu nadir olarak görülmektedir. Siyanoz bulunan altı günlük erkek bebeğin ekokardiyografik incelemesinde büyük damarların transpozisyonu, ventriküler septal defekt ve aortik ark interapsiyonu saptandı. İndirekt bilirubini yüksek olan hasta üç gün sonra ameliyata alındı. Tek oturumda posterolateral torakotomi ve midsternotomi insizyonu yaklaşımlarıyla tam düzeltme yapıldı, derin hipotermi ve total sirkülatuvar arreste gerek duyulmadı.

Büyük damarların transpozisyonu, ventriküler septal defekt ve aortik ark interapsiyonu bulunan hastada tek oturum ve iki ayrı insizyonla cerrahi tedavi

Transposition of great arteries with ventricular septal defect and interruption of aortic arch is a rare malformation. We present a nine-day-old cyanotic male neonate whose echocardiographic assessment revealed transposition of great arteries with ventricular septal defect and interruption of aortic arch. The patient had indirect hyperbilirubinemia and was operated 3 days after admission. Complete repair was performed by a single stage operation with two incisions. With this technique the need for deep hypothermia and total circulatory arrest was abolished.

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