Mehmed YANARTAŞ, Ramesh. S KUTTY, Rober. E NADLER, JENKİNS David. P

Successful treatment of pulmonary angiosarcoma along with pulmonary endarterectomy and pulmonary valve replacement

Pulmoner endarterektomi (PEA), kronik tromboembolik pulmoner hipertansiyon (KTEPH) hastalarında etkili bir tedavi seçeneğidir. Pulmoner anjiyosarkomun (PS) semp- tomları, benzer radyolojik bulgular göstererek KPTEHyi taklit edebilir. Bu yazıda, ilerleyici nefes darlığı ve anji- nası olan 69 yaşında erkek bir olgu sunuldu. Klinik ve radyolojik muayenede pulmoner kapağa uzanan ve ayırıcı tanıda PS olabileceğini gösteren bir kitle ile birlikte, pul- moner hipertansiyon tespit edildi. Pulmoner endarterek- tomi cerrahisi ile eş zamanlı pulmoner kapak replasmanı yapıldı. Histolojik incelemede, PS tanısı doğrulandı. Hasta adjuvan kemoterapi için yerel bir onkoloji kliniğine yönlendirildi.

Pulmoner anjiyosarkomun pulmoner endarterektomi ve pulmoner kapak replasmanı ile birlikte başarılı tedavisi

Pulmonary endarterectomy (PEA) is an effective treatment of choise for patients with chronic thromboembolic pulmonary hypertension (CTEPH). Symptoms of pulmonary angiosarcoma (PS) can mimic CTEPH, showing similar radiological findings. In this article, we report on a 69-year-old male case with progressive dyspnea and angina. Clinical and radiographic examination revealed pulmonary hypertension with a mass extending to the pulmonary valve, indicating potential PS in the differential diagnosis. A pulmonary valve replacement was performed concurrently with PEA surgery. Histological examination confirmed the diagnosis of PS. The patient was referred into a local oncology service for adjuvant chemotherapy. Key words:

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