Abdullah ÖZYURT, Özge PAMUKÇU, Hakan CEYRAN, Nazmi NARİN, Kazım ÜZÜM, Mustafa ARGUN, Ali BAYKAN

Sol hemitrunkuslu bir infantta aşamalı cerrahi tedavi

Sol hemitrunkus (sol pulmoner arterin aort kökeninden ayrılma anomalisi) sağ hemitrunkusa göre daha nadir görülür. Fallot tetralojisi ile sol hemitrunkus birlikteli- ğinde sol pulmoner yatakta erken gelişebilecek pulmoner vasküler obstrüktif hastalığı önlemek için erken tanı çok önemlidir. Bildiğimiz kadarıyla, literatürde, Fallot tetralojisi ve sol hemitrunkus birlikteliğinde ilk dekatta yapılan ve yaşayan beş sol hemitrunkuslu olgu mevcuttur. Aşamalı cerrahi yapılarak tam düzeltme sağlanan herhan- gi bir pediatrik olgu literatürde henüz bildirilmemiştir. Bu yazıda, palyatif sol pulmoner band ameliyatının ardından total tamir ile aşamalı düzeltme cerrahisi yapılan geç tanı konulmuş Fallot tetralojili ve sol hemitrunkuslu bir yaşında kız çocuğu sunuldu.

Staged surgical treatment in an infant with left hemitruncus

Left hemitruncus (aortic anomalous origin of the left pulmonary artery) is relatively rare than the right hemitruncus. Early diagnosis is critical to prevent early occurrence of pulmonary vascular obstructive disease in the left pulmonary bed in patients with tetralogy of Fallot presenting with left hemitruncus arteriosus. To the best of our knowledge, there are only five surviving cases with left hemitruncus and tetralogy of Fallot who were operated in the first decade of life in the literature. Any pediatric case undergoing staged surgery with full recovery has not been reported yet in the literature. In this article, we report a one-year-old girl with tetralogy of Fallot and left hemitruncus with a late diagnosis who underwent staged correction surgery with palliative left pulmonary artery banding followed by total repair.

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