Vikasdeep GOYAL, Sanjeev DEVGARHA, Chandraprakash SRIVASTAVA

Atrial and visceral situs inversus with congenitally corrected transposition of the great arteries in a patient with dextrocardia, ventricular septal defect and pulmonary stenosis: A rare presentation

Bu makalede, 16 yaşındaki bir kız hastada nadir bir doğuştan düzeltilmiş büyük damar transpozisyonu olgusunu sunuyoruz. Hastada dekstrokardinin eşlik ettiği atriyal ve visseral situs inversus ve aynı zamanda pulmoner stenozlu ventriküler septal defekt vardı. Siyanöz ve egzersize bağlı dispne başlıca semptomlardı. Ventriküler septal defekt, mitral kapaktaki sol taraflı morfolojik sağ atriyum üzerinden kapatıldı. Cerrah, hastanın sol tarafından ameliyatı gerçekleştirdi. Pulmoner arter, perikardiyal yama ile büyütüldü.

Atriyal ve visseral situs inversusla birlikte doğuştan düzeltilmiş büyük damar transpozisyonu olan bir hastada dekstrokardi, ventriküler septal defekt ve pulmoner stenoz birlikteliği: Nadir bir olgu

In this article, we present a-16-year-old female case of congenitally corrected transposition of the great arteries. The patient had atrial and visceral situs inversus with dextrocardia, and also ventricular septal defect with pulmonary stenosis. Presenting symptoms were cyanosis and dyspnea on exertion. The ventricular septal defect was closed through the left-sided morphological right atrium across the mitral valve. The surgeon operated from the left side of the patient. The pulmonary artery was augmented with a pericardial patch.

PDF

___

1. Allwork SP, Bentall HH, Becker AE, Cameron H, Gerlis LM, Wilkinson JL, et al. Congenitally corrected transposition of the great arteries: morphologic study of 32 cases. Am J Cardiol 1976;38:910-23.
2. Connelly MS, Liu PP, Williams WG, Webb GD, Robertson P, McLaughlin PR. Congenitally corrected transposition of the great arteries in the adult: functional status and complications. J Am Coll Cardiol 1996;27:1238-43.
3. Anderson RC, Lillehei CW, Lester RG. Corrected transposition of the great vessels of the heart: a review of 17 cases. Pediatrics 1957;20:626-46.
4. Mitropoulos FA, Kanakis M, Vlachos AP, Lathridou P, Tsaoussis G, Georgiou G, et al. Congenitally corrected transposition of the great arteries: surgical repair in adulthood. Ann Thorac Surg 2007;83:672-4.
5. Sirin BH, Kurdal AT, Iskesen I. Congenitally corrected transposition of the great arteries plus dextrocardia operated with an unusual operative technique. Thorac Cardiovasc Surg 2008;56:367-9.
6. Schmidt M, Theissen P, Deutsch HJ, Dederichs B, Franzen D, Erdmann E, et al. Congenitally corrected transposition of the great arteries (L-TGA) with situs inversus totalis in adulthood: findings with magnetic resonance imaging. Magn Reson Imaging 2000;18:417-22.
7. Attie F, Cerda J, Richheimer R, Chávez-Domínguez R, Buendia A, Ovseyevitz J, et al. Congenitally corrected transposition with mirror-image atrial arrangement. Int J Cardiol 1987;14:169-75.
8. Sharma R, Talwar S, Marwah A, Shah S, Maheshwari S, Suresh P, et al. Anatomic repair for congenitally corrected transposition of the great arteries. J Thorac Cardiovasc Surg 2009;137:404-412.e4.