Koklear implantasyon: İnkomplet partisyon tip III üzerine olgu sunumu

İnkomplet partisyon İP tip III anomalisi X-bağımlı deformite, İP tip III iç kulağın nadir bir malformasyonudur. Bu hastalarda koklear implant cerrahisi başarıyla uygulanabilir. Bu olgu sunumunda, İP tip III anomalisi ve şiddetli sensörinöral işitme kaybı olan hastalarda koklear implantasyon ile ilgili problemler tartışıldı. Koklear implantasyon bu hastalar için iyi bir tercihtir. Ancak İP tip III anomalisi diğer iç kulak anormalliklerine ek olarak bazı olağandışı riskler oluşturabilir. Dolayısıyla, cerrah bunları bilmeli ve hastayı ve ebeveynleri olası komplikasyonlar hakkında bilgilendirmeye hazır olmalıdır

Anahtar Kelimeler:

Koklear implant, inkomplet partisyon tip III anomalisi, iç kulak anomalisi

Cochlear implantation: case report on incomplete partition type III

Incomplete partition IP type III anomaly X-linked deformity, IP type III is a rare malformation of the inner ear. In these patients, cochlear implant surgery can be performed successfully. In this case report, we discussed the problems regarding cochlear implantation in patients with IP type III anomaly and profound sensorineural hearing loss. Cochlear implantation is a good choice for these patients. However, IP type III anomaly may pose some unusual risks in addition to other inner ear abnormalities. Therefore, the surgeon should be aware of these and must be ready to inform the patient and parents about possible complications.

Keywords:

Cochlear implant, incomplete partition type III anomaly, inner ear anomaly,

PDF

___

Jensen J. Malformations of the inner ear in deaf children. Acta Radiol Suppl 1969;286:1-97.
Tucci DL, Telian SA, Zimmerman-Phillips S, Zwolan TA, Kileny PR. Cochlear implantation in patients with cochlear malformations. Arch Otolaryngol Head Neck Surg 1995;121:833-8.
Mangabeira-Albernaz PL. The Mondini dysplasia- -from early diagnosis to cochlear implant. Acta Otolaryngol 1983;95:627-31.
Jackler RK, Luxford WM, House WF. Congenital malformations of the inner ear: a classification based on embryogenesis. Laryngoscope 1987;97(3 Pt 2 Suppl 40):2-14.
Phippard D, Heydemann A, Lechner M, Lu L, Lee D, Kyin T, et al. Changes in the subcellular localization of the Brn4 gene product precede mesenchymal remodeling of the otic capsule. Hear Res 1998;120:77-85.
Sennaroglu L, Saatci I. A new classification for cochleovestibular malformations. Laryngoscope 2002;112:2230-41.
Sennaroglu L. Cochlear implantation in inner ear malformations--a review article. Cochlear Implants Int 2010;11:4-41.
Park AH, Kou B, Hotaling A, Azar-Kia B, Leonetti J, Papsin B. Clinical course of pediatric congenital inner ear malformations. Laryngoscope 2000;110:1715-9.
Weber BP, Dillo W, Dietrich B, Maneke I, Bertram B, Lenarz T. Pediatric cochlear implantation in cochlear malformations. Am J Otol 1998;19:747-53.
Tullu MS, Khanna SS, Kamat JR, Kirtane MV. Mondini dysplasia and pyogenic meningitis. Indian J Pediatr 2004;71:655-7.
Battmer R, Pesch J, Stöver T, Lesinski-Schiedat A, Lenarz M, Lenarz T. Elimination of facial nerve stimulation by reimplantation in cochlear implant subjects. Otol Neurotol 2006;27:918-22.