Curry Jones Sendromlu Hastada Preoperatif Anestezi Yönetimi

Curry-Jones Sendromu (CJS), kraniyofasiyal malformasyonlar, polisindaktili, yamalı deri lezyonları ,göz ve bağırsak anormallikleri ile karakterize nadir görülen bir hastalıktır. Curry Jones Sendromu SMO gen mutasyonuna bağlı olmaktadır. Biz vakamızda Curry Jones Sendrom tanılı çocuk hastaya planlanan operasyon için preoperatif anestezi yaklaşımından bahsettik.

Anahtar Kelimeler:

Curry Jones Sendrom, anestezi, çocuk

Perioperative anesthesia management in a patient with curry jones syndrome

Keywords:

Curry-Jones Syndrome, anesthesia, child,

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