Münevver TÜRKMEN, Arzu TANINMIŞ, S. Ayvaz AYDOĞDU, C. Zafer KARAMAN, Harun GÜRSOY

YENİDOĞANDA NADİR BİR SOLUNUM SIKINTISI NEDENİ: AKCİĞERLERİN KONJENİTAL KİSTİK ADENOMATOİD MALFORMASYONU

Yenidoğan döneminde solunum sıkıntısı ile karşılaşıldığında, nadir olarak rastlansa da, akciğerlerin konjenitalanomalilerinin hatırlanması amacıyla bu olgu sunulmuştur. Konjenital kistik adenomatoid malformasyon nadirrastlanan ancak hayatı tehdit eden bir akciğer anomalisidir. Yaklaşık 25000 doğumda bir görülür. Doğumun ilksaatlerinde başlayan solunum sıkıntısı nedeni ile yenidoğan yoğun bakım ünitesine sevk edilen olgunun fizikmuayenesinde solunum sıkıntısı bulguları ve pektus ekskavatus deformitesi mevcuttu. Akciğer grafisinde, solakciğerde kaba retikülogranüler görünümü, toraks bilgisayarlı tomografisinde (BT) sol akciğerde parankimiçerisinde çok sayıda, yaygın, değişik boyutta hava kisti saptandı. BT ve akciğer grafi bulguları ile konjenitalkistik adenomatoid malformasyon Tip III ile uyumlu olarak değerlendirildi. Olgu yaşamının onuncu günündemekanik ventilatörde izlenmekte iken kaybedildi

Anahtar Kelimeler:

Konjenital kistik adenomatoid malformasyon, yenidoğan, solunum sıkıntısı

The Rare Cause of Respiratory Distress in Newborn: Congenital Cystic Adenomatoid Malformation of Lungs

The aim of presenting this case is that; the congenital lung abnormalities are rare, but important of differential diagnosis in newborn respiratory distress.The congenital cystic adenomatoid malformation is a rare but potentially life-threatening pulmonary anomaly. It is reported 1 in 25000 pregnancies. Respiratory distress, pectus excavatus deformity were detected in the physical examination of the infant who was accepted to our newborn intensive care unit in the first hours of his life. In the chest X-ray there was reticulogranular appearance in left lung and there was multiple, diffuse cysts which were in different size in lung parenchyma in the computerize tomography (CT) examination. The signs on the CT and X-ray were accepted as a congenital cystic adenomatoid malformation type III. The case died at his tenth day of the life during assisted mechanical ventilation.

Keywords:

Congenital cystic adenomatoid malformation, newborn, respiratory distress,

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