Meltem USLU, Göksun KARAMAN, Ekin ŞAVK, Neslihan ŞENDUR, Eylem YILMAZ

AYDIN'DA BEHÇET HASTALIĞI DENEYİMİ: 67 HASTANIN RETROSPEKTİF DEĞERLENDİRİLMESİ

AMAÇ:Bu çalışmada Adnan Menderes Üniversitesi Tıp Fakültesi Dermatoloji AD'da izlenen Behçethastalarının demografik ve klinik özelliklerinin belirlenmesi amaçlandı.GEREÇ ve YÖNTEM:Çalışmaya uluslararası Behçet hastalığı tanı kriterlerini dolduran 67 hasta dahil edildi.Hastaların dosya bilgileri incelendi ve veriler SPSS 14 programı kullanılarak analiz edildi.BULGULAR:Yaşları 16 ile 61 arasında değişen hastaların yaş ortalaması 35.7±10.5'ti ve erkek/kadın oranı1.48:1 idi. Hastalığın ilk semptomunun başlama yaşı ortalaması 27.1±9.3, Behçet hastalığı tanısını alma yaşıortalaması 32.4±9.6'ydı. Oral ülserler (%100) ve genital ülserler (%97.0) hastalığın en sık bulguları idi. Bunlarıpapülopüstüler döküntü (%72.3), paterji pozitifliği (%50.8) eritema nodozum (%38.8), eklem tutulumu (%23.9),göz tutulumu (%21.5) ve tromboflebit (%9.1) izledi. Tromboflebit anlamlı olarak erkeklerde daha fazla görüldü(p=0.03).SONUÇ:Aydın'da tek merkezli olarak Dermatoloji kliniğinde izlenen Behçet hastalarının verileri sunuldu.Mukokutanöz bulguların ön planda olduğu hastaların hiçbirinde şiddetli tutulum izlenmedi

Anahtar Kelimeler:

Behçet hastalığı, epidemiyoloji, Türkiye

Behcet's Disease Experience in Aydin: Retrospective Evaluation of 67 Patients

We aimed to investigate the demographical and clinical features of patients with Behçet's disease followed up inAdnan Menderes University Medical Faculty, Dermatology Department. Sixtyseven patients who fullfilled the diagnostic criteria of the International Study Group for Behçet's Disease were included to the study. Patients records were investigated and analysed by using SPSS 14 programme. Patient's age range was between 16-61, mean age was 35.7±10.5 and male/female ratio was 1.48:1. The mean age at the first symptom of the disease was 27.1±9.3, and mean age of the diagnosis of Behçet's disease was 32.4±9.6. Oral ulcers (100.0%) and genital ulcers (97.0%) were the most common findings of the disease. These were followed by papulopustular lesions (72.3%), pathergy positivity (50.8%) erythema nodosum (38.8%), articular involvement (23.9%), eye involvement (21.5%) and thrombophlebitis (9.1%). Thrombophlebitis was seen significantly more frequently in male patients than females (p=0.03). The data of patients with Behçet's disease who were followed up in a Dermatology clinic in Aydin were presented as a one centered study. Major findings were mucocutaneous ones and none of the patients had the severe involvement of the Behçet's disease

Keywords:

Behçet's disease, epidemiology, Turkey,

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