Nil ÇULHACI, Nesibe Kahraman ÇETIN, İzzet KOÇAK

MULTİLOKÜLER KİSTİK RENAL HÜCRELİ KARSİNOM

Multiloküler kistik renal hücreli karsinom kistik renal neoplazmların karakteristik histolojik bulguları olan veçok iyi prognoza sahip nadir görülen bir alt tipidir. Multiloküler kistik renal hücreli karsinom tüm renaltümörlerin %1'ini oluşturur ve çeşitli boyutlarda, seröz veya hemorajik sıvı ile dolu, grade I nükleer özelliklergösteren berrak hücrelerle döşeli düzensiz, ince duvarlı fibröz septalarla ayrılmış kistlerle karakterlidir. Tümörrekürrensi veya metastazı bildirilmemiştir. Bu tümörün kistik nekroz gösteren unilokuler veya multilokuler kistikrenal hücreli karsinomdan ayrılması önemlidir. Bu makalede, multiloküler kistik renal hücreli karsinom tanısınedeniyle nefrektomi uygulanan 53 yaşında erkek hasta sunulmaktadır

Anahtar Kelimeler:

Renal hücreli karsinom, multiloküler kistik renal hücreli karsinom, kistik renal tümörler

Multilocular cystic renal cell carcinoma

Multilocular cystic renal cell carcinoma is an uncommon subtype of cystic renal neoplasms with characteristic histologic findings and a good prognosis. Multilocular cystic renal cell carcinoma, accounts for 1% of all renal tumors and it is characterized by variably sized, serous or hemorrhagic fluid filled cysts separated by irregular, thin-walled, fibrous septa covered with clear cells showing grade I nuclear features. No tumor recurrences or metastasis have been reported. It is important to distinguish this tumor from unilocular or multilocular cystic renal cell carcinoma showing cystic necrosis. Here we report on a 53-year-old man who underwent nephrectomy for multilocular cystic renal cell carcinoma.

Keywords:

Renal cell carcinoma, multilocular cystic renal cell carcinoma, cystic renal tumors,

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