Eray COPCU, Nazan SİVRİOGLU, Yücel ÖZTAN

DOĞUMSAL ÇİFT DUDAK DEFORMİTESİ: 8 OLGUNUN SUNUMU

Doğumsal çift dudak nadir rapor edilen, ancak sık görülen bir anomalidir. Bu klinik durum sıklıkla izole birdeformite olarak görülse de, bir sendromun parçası da olabilir. Sıklıkla erkeklerde görülen ve patogeneziembriyolojik gelişimdeki defektlerle açıklanmaya çalışılan bu deformite ile ilgili olarak literatürde yirmiden azsayıda yayınlanmış çalışma vardır. Bizim çalışmamızda, kadın erkek sayısı eşit olup olguların hepsi estetikyakınmalarından dolayı doktora başvurmuşlardır. Olguların hepsine lokal anestezi altında eliptik eksizyonyapılmıştır. Alınan cerrahi örneklerin patolojik incelemeleri normal dudak mukozası olarak rapor edilmiştir.Olguların hiçbirinde post-operatif erken yada geç komplikasyon görülmeyip istenilen kozmetik sonuç eldeedilmiştir. Bir olguda parsiyel çift dudak deformitesi saptanmış olup, bilgilerimize göre literatürde parsiyel çiftdudak deformitesine ait bir yayın yoktur. Sonuç olarak bu çalışmada, doğumsal çift dudağa sahip toplam 8 olgusunulmuş ve bu deformitenin etyolojisi, görülme sıklığı ve tedavi yöntemleri literatürdeki bulgular eşliğindetartışılmıştır

Anahtar Kelimeler:

Çift dudak, doğumsal, deformite, oral, eliptik eksizyon, parsiyel

Congenital Double Lip Deformity: Presentation of Eight Cases

Although congenital double lip deformity is not an uncommon condition, this deformity was presented rarely in the literature. Congenital double lip deformity may be present either as an isolated anomaly or a component of a syndrome. However less than twenty reports were presented in the literature, males were affected predominantly and pathogenesis of this deformity was explained by the embryological defects. In our study male to female ratio was equal and all patients were operated since the aesthetical reason. Elliptical excision was performed under the local anesthesia in all patients. All specimens were evaluated pathological and reported as “normal lip mucosa”. There were no early or late post-operative complication and aesthetical results were achieved in all patients. One case of our patients had partial congenital lip deformity, best of our knowledge; there was no data about the partial congenital lip deformity. Finally, in this study we present eight cases with congenital double lip and discuss the etiology, incidence and treatment modalities according to the data presented in the literature.

Keywords:

Double lip, congenital, oral, elliptical excision, partial,

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