An artificial nail disorder

Submukazal (Meissner) ve myenterik (Auerbach) nöral pleksusların konjenital aganglionozisi olan Hirschsprung hastalığında esas olarak değişik uzunluktaki rektosigmoid veya rektum segmenti etkilenir. Olguların çoğunda hastalık neonatal dönemde manifest hale gelirken, nadiren de olsa ilk olarak erişkin yaşta tanı alır. Kronik kabızlık öyküsü ve uygun radyolojik bulguları olan hastalarda erişkin Hirschsprung hastalığı tanısından şüphelenilmelidir.

faktisyel tırnak hastalığı

Hirschsprung’s disease is a congenital aganglionosis of the submucosal (Meissner) and myenteric (Auerbach) neural plexuses principally affecting the rectosigmoid or rectal segments of varying length. Most cases become manifest during the neonatal period, but in rare instances, the disease is initially diagnosed in adult patients. The diagnosis of adult Hirschsprung’s disease should be suspected in patients with a history of chronic constipation and appropriate radiologic findings.

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