ÇOCUKLUK ÇAĞINDA NADİR BİR PULMONER TÜMÖR: RABDOMYOSARKOMA
Lokal olarak yaygın olan tümör, 4 kür kemoterapi sonrası çekilen bilgisayarlı tomografide minimal regresyon gösterdi. Kemoterapinin 12. haftasında halen hayati yapılara yaypışıklık gösteren tümörün lokal kontrolünü sağlamak amacı ile radyoterapi uygulandı. Radyoterapiyi takiben 3 VAC (vinkristin, aktinomisin D, siklofosfamid) kürü daha verildikten sonra tümörün progresyon göstermeye devam etmesi nedeni ile tedavi sonlandırıldı. Tanıdan 9 ay sonra hasta kaybedildi. Primer pulmoner rabdomyosarkomun prognostik özellikleri tartışıldı; persistan pulmoner semoptomları ve göğüs röntgeninde anormallikleri olan çocukların ayırıcı tanısında akla gelmesi gerektiği vurgulandı.Anahtar Kelimeler: Malignite, Göğüs, Rabdomyosarkoma, Çocukluk
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