Alper URAL, Fatma BİLGEN, Abdülkadir Yasir BAHAR, Mehmet BEKERECİOĞLU

Nadir Karşılaşılan Sık Karıştırılan Bir Tümör: Lenfanjiyoma Sirkumskriptum (Yüzeyel Lenfatik Malformasyon)

Lenfanjiyoma Sirkumskriptum yüzeyel lokalize bir lenfanjiom varyantıdır. Karakteristik klinik prezentasyonu kümelenmiş vezikül yada papüloveziküller şeklindedir. Çoğu lenfanjiyomlar konjenital gelişmesine rağmen erişkin yaşlarda da görülebilmektedir.Bu yazıda kliniğimizde tedavi ettiğimiz sağ aksiller bölgede ve meme başında nüks etmiş bir lenfanjioma sirkumskriptum olgusu sunulmuştur. Lenfanjiyoma sirkumskriptum hastalığının tekrarlama ve ikincil malignite gelişebilmesi nedeniyle doğru tanı ve tedavi çok önemlidir. Çeşitli tedavi seçenekleri olmasına karşın özellikle rekürren vakalar için cerrahi eksizyon altın standart olup hastaların takibe alınması elzemdir.

Anahtar Kelimeler:

lenfanjioma sirkumskriptum, vasküler tümörler, yüzeyel lenfatik malformasyon

A Rarely Encountered, Frequently Misleading Tumor: Lymphangioma Cirkumscriptum (Superficial Lymphatic Malformation)

Lymphangioma Circumscriptum is a superficially localized variant of lymphangioma. The characteristic clinical presentation is a grouping of vesicles or papulovesicles. Though most lymphangiomas develop congenitally, the lymphangioma circumscriptum subtype is known to present also in adults.We report a case of recurrent lymphangioma circumscriptum on the right axillary and periareolar area treated in our clinics. Accurate diagnosis and treatment is crucial in cases of lymphangioma circumscriptive because of the possibility of recurrence of this disease and the possibility of developing malignancy secondarily. Besides the various treatment modalities, surgical excision is the gold standard especially for recurrent cases and the patients need to be followed-up.

Keywords:

circumscriptum, lymphatic malformation, vascular tumors,

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