Psikotik Belirtili Manik Hecme ile Başvuran Bir Fahr Hastalığı Vakası

Fahr Hastalığı bazal ganglionların bilateral, simetrik veidiyopatik kalsifikasyonudur. Üç temel özelliğinden birikalsifikasyon, diğer ikisi ise psikiyatrik semptomlar vehareket bozukluklarıdır. Psikiyatrik bulgular arasında duygudurum bozuklukları, psikotik bozukluklar, obsesyonlar vekişilik değişiklikleri görülür. Bu bulgular nörolojik bulgularaeşlik edebildiği gibi nadiren izole olarak da ortaya çıkabilir.Cummings ve arkadaşları psikotik semptomlarla belirtiveren erken başlangıçlı form ve demans ile birliktehareket bozuklukları olan geç başlangıçlı form olarak ikiayrı tip tanımlamışlardır. Bu yazıda obsesyonla başlayıppsikotik belirtili manik hecme ile seyreden, atipik psikiyatrik klinik tablosu nedeniyle etyolojisi araştırılan ve yapılangörüntüleme yöntemleri ile ileri tetkikler neticesinde FahrHastalığı olduğu saptanan bir vaka tartışılmıştır. Bu vakanın, bazal ganglionların psikiyatrik yansımaları ve psikiyatrihastalarına yaklaşım açısından bilime katkıda bulunacağıdüşünülmektedir.

A Fahr s Disease case presented with psychotic manic epizode

Fahr s Disease is bilateral, symmetric, and idiopathiccalcification in basal ganglia. Calcification is one of thethree basic features. The others are psychiatric symptomsand movement disorders. Psychiatric symptoms are moodchanges, psychosis, obsessions, and personality changes.These symptoms appear not only with neurological symptoms but also rarely isolated. Cummings and friendsdescribed two types of Fahr s Disease. Presented withpsychosis is early-onset type and typically manifesteddementia and motor system disorders is late-onset type .In this case report we discussed a case that begun withobsession and then manic episode with psychotic symp- toms, considered organic etiology because of atypical psychiatric clinical appearance, diagnosed as Fahr s Disease asa result of neuroimaging techniques and further investigations. We think that this case will contribute to literatureabout psychiatric aspects of basal ganglia and approach tothe psychiatric patients.

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