Ersin KÖKSAL, Nurullah YILMAZ, Cengiz KAYA, Yasemin ÜSTÜN, Ali ŞAHİNOĞLU, Fatih ÖZKAN

Epidermolizis Büllozalı Hastada Anestezik Yaklaşım: Olgu Sunumu

Epidermolizis bülloza (EB); cilt ve mukozalarda frajilite ve bül oluşumuyla karakterize bir hastalıktır. Özellikle havayolundaki büller, yapılacak girişimlere bağlı yeni bül oluşumu anestezi yönetimini güçleştirir. Bu sunumda rekonstrüktif cerrahi planlanan, 6 yaşındaki, EB tanılı olgunun anestezik yönetimi anlatıldı. Anestezi ve analjezi optimal monitörizasyon ve girişim sonrası intravenöz (iv) yoldan sağlandı. Ventilasyon ise orofaringeal lezyonların varlığı ve ağız açıklığındaki kısıtlılık nedeniyle yüz maskesi ile gerçekleştirildi. Yeni lezyon veya komplikasyon oluşmadı

Anahtar Kelimeler:

anestezi; epidermolizis bülloza; preoperatif değerlendirme

Anesthetic Approach to a Patient with Epidermolysis Bullosa: A Case Report

Epidermolysis Bullosa (EB) is characterized by fragility and formation of blisters in the skin and mucosal membranes. Due to blisters on the airway and occurring new blisters as a result of anesthetic or surgical procedures may complicate anesthesia management. In this case report, we present the anesthetic approach of a 6 years old case with EB who underwent reconstructive surgery. After premedication and optimal monitorization, intravenous (IV) anesthesia and analgesia was administered. Associated with the oropharyngeal lesions and limitation to reach an adequate mouth opening, we preferred the facemask to maintain ventilation. Neither new lesions nor complications were detected during or after surgery.

Keywords:

anesthesia; epidermolysis Bullosa; preoperative evaluation,

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