Yasin ÇINAR, Şeyhmus ARI, Muhammed ŞAHİN, İhsan ÇAÇA, Alparslan ŞAHİN, Abdullah Kürşat CİNGÜ

Trigeminal nerve involvement in congenital insensitivity of pain with anhidrosis

Konjenital ağrı duyarsızlığı ve anhidrosis birlikteliği (CIPA)kornea anestezisinin nadir görülen bir nedenidir. Burada, trigeminal anestezi ile ilişkili olarak ağrısız kornea epiteldefekti, ciddi kuru göz belirtileri, süt dişlerinin erken kaybıve üst dudakta ağrısız fissür ve periferik ağrı duyarsızlığı ile ilişkili olarak ekstremitelerde ağrısız yaraları bulunan bir CIPA olgusunu sunmayı amaçladık.

Doğumsal ağrı duyarsızlığı ve trigeminal sinir tutulumu

Congenital insensitivity to pain with anhidrosis (CIPA) isa rare cause of corneal anesthesia. Here, we report acase of CIPA with clinically prominent features of severedry eye symptoms with painless corneal epithelial defect,early loss of primary teeth and a painless fissure on herupper lip in association with trigeminal anesthesia, andpainless wounds on extremities.

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