İlker Öngüç AYCAN, Gönül Ölmez KAVAK, Zeynep Baysal YILDIRIM, Hüseyin TURGUT

Anesthetic management in VACTERL syndrome

Çoklu konjenital malformasyonlardan dolayı VACTERL sendromunda anestezi yönetimi vertebra, kardiyak, trakea-özefageal, renal ve ekstremite anomalileri nedeniyle bir çok problemi içermektedir. Bu yazıda trakeo-özefageal fistül nedeniyle opere olan VACTERL sendromlu hastamızdaki anestezi öncesi değerlendirme, premedikasyon, anestezi indüksiyonu ve devamı ile postoperatif izlemi içeren anestezi yönetimimizi sunmayı amaçladık.

VACTERL sendromunda anestetik yaklaşım

VACTERL Syndrome consists of many problems regarding to anesthesia management due to multiple congenital malformations which may include vertebral, cardiac, trachea-osephageal, renal and limb anomalies. Here we present our anesthetic management -in terms of preanesthetic evaluation, premedication, induction and maintenance of anesthesia and postoperative follow up- in a newborn patient with VACTERL Syndrome undergoing tracheo-eosophagial fistula operations.

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Solomon BD. VACTERL/VATER association. Orphanet 2011;6:1-12.
Yıldız TŞ, Özcan D, Solak M, Toker K. VACTERL Syn- drome and Anesthesia. J Anesth 2012;20:174-175.
Luce V, Mercier FJ, Benhamou D. Anesthetic manage- ment for a parturient affected by the VACTERL asso- ciation. Anesth Analg 2004;98:870-878.
Khatavkar SS, Jagtap SR. Anaesthetic management of cataract surgery in VACTERL syndrome case report. Indian J Anaesth 2009;53:94-97.
Mariano ER, Chu LF, Albanese CT, Ramamoorthy C. Successful thoracoscopic repair of esophageal atresia with tracheoesophageal fistula in a new- born with single ventricle physiology. Anesth Analg 2005;101:1000-1002.
Barois J, Tourneux P. Ketamine and atropine decrease pain for preterm newborn tracheal intubation in the delivery room: an observational pilot study. Acta Pae- diatr 2013 Sep 10. doi: 10.1111/apa.12413.
Rittler M, Paz JE, Castilla EE. VACTERL association, epidemiologic definition and delineation. Am J Med Genet 1996;63:529-536.
Hatemi AC, Gursoy M, Ceviker K, et al. Ventricular septal defect closure in a patient with VACTERL Syn- drome: anticipating sequelae in a rare genetic disor- der. Tex Heart Inst J 2008;32: 203-205.