Mehmet YILMAZER, Gülengül KÖKEN, Figen Kır ŞAHİN

Fetal sakrokoksigealteratom: Prenatal tanı ve yönetim

Sakrokoksigeal teratom (SKT) germ hücre kaynaklıdır ve en sık görülen fetal tümördür. SKT'lu hastalarda yüksek debili kalp yetersizliği, preterm doğum, anemi, distosi ve tümör rüptürü nedeniyle perinatal mortalite ve morbidite yüksektir. Yirmi dört yaşındaki hastamız, 30. hafta gebelikte fetal kitle nedeniyle kliniğimize sevk edildi. Ultrasonografide fetal sakral bölgede sakrokoksigeal teratomla uyumlu solid ağırlıklı kitle ve polihidroamnios saptandı. Takiplerimizde maternal mirror sendromu gelişmesi nedeniyle 31+4 günlük gebelikte sezaryen ile doğum yaptırıldı.Bu yazıda prenatal tanı konmuş sakrokoksigeal teratomlu bir olgunun gebelik takibi ve doğum şekline ilişkin yaklaşımlar tartışılmıştır.

Fetal sacrococcygeal teratoma: Prenatal diagnosis and management

Sacrococygeal teratoma (SCT), a germ cell tumor, is the most common fetal neoplasm. Patients with SCT have high mortality and morbidities due to heart failure, preterm delivery, anemia, distocia, and tumor rupture. A24 year-old woman was referred to our clinic due to a fetal mass at the 30th week of gestation. Ultrasonography revealed polyhydramniosis and a solid mass lesion in the sacral region which is consistent with sacrococcygeal teratoma. In the follow-up, maternal mirror syndrome developed, therefore, the pregnancy was terminated by cesarean section at the 31th week and 4 days.In this report we presented a case of sacrococcygeal teratom prenatally diagnosed and discussed the management options for the delivery

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