Gökçe ŞİMŞEK, lrem PAKER, Mehmet ŞAHAN, Ömer SERİN, İstemihan AKIN

Pediatrik Hastada Parotisin Mukoepidermoid Karsinomu: Olgu Sunumu

Mukoepidermoid neoplazmlar, tüm pediatrik tükürük bezi tümörlerinin üçte birini oluşturmaktadır ve en sık parotis glandında izlenir. Mukoepidermoid karsinomlar histolojik diferansiasyon derecesine göre düşük, orta ve yüksek dereceli tümörler olarak üçe ayrılırlar. Düşük gradeli tümörler benign gibi davranmalarına rağmen lokal invazyon ve metastaz yapma potansiyelleri vardır. Hastalığın klinik evresi ve tümörün histolojik derecesi prognozu belirleyen ana faktörlerdir. Tedavide fasiyal sinir korunarak total parotidektomi yapılır. Pediatrik yaş grubunda sekonder malignite riski ve mandibula gelişimi açısından primer tedavide radyoterapi tercih edilmez. Bu yazıda sağ parotis glandında düşük gradeli mukoepidermoid karsinom saptanan yaşında erkek hasta sunuldu. Pediatrik tükürük bezi maligniteleri olgu sunumuyla beraber güncel literatür bilgileri eşliğinde tartışıldı.

Mucoepidermoid Carcinoma of The Parotid in Pediatric Patient: Case Report

Mucoepidermoid tumors consist one third of all pediatric salivary gland neoplasm. The most common location of the tumor is parotidgland. These tumors are classified as low, intermediate and high grade according to the degree of histological differentiation. Low gradetumors generally behave as benign pathologies, although local invasion and metastasis can be rarely seen. Clinical stage and histologicalgrade are the main prognostic factors. Total parotidectomy with facial nerve sparring is the treatment of choice in pediatric cases.Radiotherapy is generally avoided since the risk of secondary malignity and impaired development of mandible in this subgroup of cases. Inthis article, 9-year-old boy with low grade mucoepidermoid carcinoma in the right parotid gland was presented. Pediatric salivary glandmalignancies were discussed with the case report along with the current literature.

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