Serdal ÇELEBİ, A. Şahap KÜKNER, Lokman ASLAN, Ahmet BAL

A female patient with Parry-Romberg syndrome: A case report

PRS'u etyolojisi belli olmayan, yüzün bir yarısında derialtı yağ ve diğer dokuların kendiliğinden yavaş seyirli ilerleyici atrofisi ile karakterize nadir görülen bir tablodur. Kliniğimizde sol progressif hemifasial atrofi nedeniyle 4 yıldır takip ettiğimiz, 40 yaşında kadın hastada oftalmik ve nörolojik bulgular gözden geçirilmiştir. Hastada, intraorbital yağ dokusu atrofisine ikincil olarak gelişen ve psödoptozisin eşlik ettiği ilerleyici enoftalmus, allopesi, poliozis, irisde heterokromi ve kırpma refleksinde kayıp saptanmıştır.

Bir kadın hastada Parry-Romberg sendromu: Olgu sunumu

A 40-year-old woman with left progressive hemifacial atrophy (Parry-Romberg syndrome/PRS) is reported. PRS is an unusual condition of unknown etiology, characterized by spontaneous and slowly progressive atrophy of the subcutaneous tissue and fat. We present the findings of a patient with PRS who was observed in our clinic for over four years. Ophthalmic and neurologic involvements are reviewed. The patient presented with progression of enophthalmos associated with pseudoptosis that occurred secondary to intraorbital fatty atrophy, alopecia, poliosis, iris heterochromia, chronic dacryocystitis and lack of blink reflex.

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