Fatma Mutlu SARIGUZEL, Bilal AYGUN, Çiğdem KARAKUKCU, Vedat ARSAV, Derya KOCER, Ahmet GODEKMERDAN

Primer Plazma Hücreli Lösemi: Nadir Bir Hastalığın Değerlendirilmesi

Plazma hücreli lösemi (PHL), plazma hücrelerini içeren agresif ve nadir görülen bir kanserdir. PHL, multle myelomanın birlikte olduğu ve olmadığı şekilde iki formu (primer, seconder) bulunmaktadır. Primer ve seconder PHL'li olguların birçok klinik özellikleri benzer olsada önemli farklılıklar bulunmaktadır. Bu olgu sunumunda primer PHL'li bir hastanın klinik, patolojik ve laboratuar bulguları incelenmiştir. Bu olgu sunumunun amacı PHL'e dikkat çekmektir.

Anahtar Kelimeler:

Plazma hücresi, primer plazma hücreli lösemi, multiple myeloma diskoid

Primary plasma cell leukemia: evaluation of a rare disease

Plasma cell leukemia (PCL) is a rare and aggressive cancer involving plasma cells. There are two forms of PCL (with or without multiple myeloma). Although patients with primary and secondary PCL share several clinical features, important differences exist. We report on a case diagnosed with primary PCL. We analyzed the clinicopathologic and laboratory features of the disease. The aim of this report is to draw attention to PCL.

Keywords:

Plasma cell, primary plasma cell leukemia, multiple myeloma,

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