Mehmet DÜZLÜ, Metin YILMAZ, Merve YILDIZ, Alper TÜRKCAN, Caner ERCAN, Recep KARAMERT

Nadir Bir Disfaji Nedeni: Hipofarengeal Rabdomiyom

Ekstra-kardiyak rabdomiyomlar iskelet kası neoplazmlarının %2’sini oluşturan iyi huylu yumuşak doku tümörleridir. Baş boyun bölgesi kaynaklı rabdomiyomlar en çok oral kavite ve farenksten köken alır. Baş boyun rabdomiyomlarında başvuru şikayetleri tümör boyutu ve lokasyonuna göre değişebilir. Temel tedavi yöntemi total cerrahi eksizyondur. Biz bu çalışmada disfaji ve boğazda takılma şikayeti ile başvuran erişkin bir hipofarenks rabdomiyomu olgusunu sunmayı ve baş boyun bölgesi kaynaklı ekstrakardiyak rabdomiyomları tartışmayı planladık.

An Unusual Cause of Dysphagia: Hypopharyngeal Rhabdomyoma

Extra-cardiac rhabdomyomas are rare benign soft tissue tumors accountingfor 2% of sk eletal muscle neoplasms. Oral cavity and pharynx are the mostcommon sites for rhabdomyomas origina ting from the head and neck region.The presenting symptom for head and neck rhabdomyomas may changeaccording to tumor size and location. The main treatment modality is totalsurgical excision.In this study, we aimed to report an adult hypopharyngealrhabdomyoma case presenting with dysphagia and globus sensation and todiscuss head and neck extra-cardiac rhabdomyomas reported in the literature.

PDF

___

Burke AP, Virmani R Cardiac rhabdomyoma: a clinicopathologic study. Mod Pathol. 1991;4 :70–4.
Vermeersch H, van Vugt P, Lemmerling M, Moerman M, De Potter C. Bilateral recurrent adult rhabdomyomas of the pharyngeal wall. Eur Arch Otorhinolaryngol. 2000;257:24-6.
Metheetrairut C, Brown DH, Cullen JB, Dardick I. Pharyngeal rhabdomyoma: a clinico-pathological study. J Otolaryngol. 1992; 21 :257–61.
Sanchez Jimenez J, Dean Ferrer A, Alamillos Granados F, et al. Adult rhabdomyoma in the masticatory area. New case presentation and review of the literature. Med Oral 2001;6:64–8.
Favia G, Lo Muzio L, Serpico R, Maiorano E Rhabdomyoma of the head and neck: clinicopathologic features of two cases. Head Neck. 2003;25:700-4.
Stringer SP, Close LG, Cohen DJ, Merkel MA, Smith HJ. Adult parapharyngeal extracardiac rhabdomyoma. Otolaryngol Head Neck Surg 1988; 10 :422–6.
Kapadia SB, Ellis GL, Frisman DM, Heffner DK, Hyams VJ, Meis JM. Adult rhabdomyoma of the head and neck: a clinicopathologic and immunophenotypic study. Hum Pathol 1993; 24 :608–17.
Stringer SP, Close LG, Merkel MA, Smith HJ, Cohen DJ. Adult parapharyngeal extracardiac rhabdomyoma. Otolaryngol Head Neck Surg 1988;10:422–6.
Pichi B, Manciocco V, Marchesi P, Pellini R, Ruscito P, Vidiri A, Covello R, Spriano G. Rhabdomyoma of the parapharyngeal space presenting with dysphagia. Dysphagia. 2008;23:202-4.
Koutsimpelas D, Weber A, Lippert BM, Mann WJ. Multifocal adult rhabdomyoma of the head and neck: a case report and literature review. Auris Nasus Larynx. 2008;35:313-7.
Liang GS, Loevner LA, Kumar P. Laryngeal rhabdomyoma involving the paraglottic space. Am J Rad 1999;174:1285 -7.
Metheetrairut C, Brown DH, Cullen JB, Dardick I (1992) Pharyngeal rhabdomyoma: a clinico-pathological study. J Otolaryngol 21 :257– 61.
Rooks JJ Jr, Cassisi NJ, Alexander RW, Smith RO. Rhabdomyoma of the pharyngeal wall. Laryngoscope. 1977;87:1046-51.
Grosheva M, Gerharz M, Bovenschulte H, Beutner D. Adult multilocular rhabdomyoma as a rare cause of dysphagia. Laryngorhinootologie. 2008;87:651-3.
Andersen CB, Elling F. Adult rhabdomyoma of the oropharynx recurring three times within 35 years. Acta Pathol Microbiol Immunol Scand [A] 1986;94:281–3.