Vahide BAYSAL, Özden ÇANDIR, Ahmet AKKAYA, Demet KESİCİ, Mehmet YILDIRIM

Late-onset neurofibromatosis (NF-7): A case report

Yayın Aralığı: Yılda 4 Sayı
Yayıncı: Gazi Üniversitesi Tıp Fakültesi

İleri yaşlarda nörofibromların gelişmesi ile karakterize olan ve nadiren malign tümöral oluşumlarla seyreden 68 yaşındaki, geç başlangıçlı nörofibromatozisli (NF-7) bir olgu sunuyoruz. Olguda nörofibromatozisin sık görülen özelliklerinden cafe au lait lekeleri, aksiller çillenme ve Lisch nodülleri yoktu.

Geç başlangıçlı nörofibromatozis (NF-7): Olgu sunumu

We present a 68-year-old man with late-onset neurofibromatosis (NF-7), a very rare form characterized by the development of neurofibromas at a later adult age and by the occasional occurrence of malignant tumors. Common characteristics, such as cafe au lait spots, axillary freckling, and Lisch nodules, were not present.

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