Ödül EĞRİTAŞ, Pınar GÖÇÜN UYAR, Ayşegül BÜKÜLMEZ, Zeren BARIŞ, Sinan SARI, Buket DALGIÇ, Figen DOĞU, Ayşe ASLAN TANA

Hyperimmunoglobulin E (Job's) syndrome and staphylococcal botryomycosis in a child

Hiperimmunglobulin E Sendromu ve botriyomikozis her ikisi de nadir görülen hastalıklardandır. Hipereozinofili ve yüksek immunoglobulin E yüksekliği ile başlangıçta idiopatik hipereozinofili tanısı almakta iken son tanısı hiperimmunglobulin E sendromu olan steroid tedavisi almakta iken kutanöz ve visseral botriyomikozis gelişmiş olan 8 yaşında bir erkek olgu bildirilmiştir.

Hiperimmunglobulin E sendromu ve stafilokokkal botryomycosis olan çocuk olgu

Hyperimmunoglobulin E syndrome and botryomycosis are both uncommon disorders. This report describes the case of an 8 year old boy in whom these two disorders coexist, who presented with hypereosinophilia, and elevated immunoglobulin E and was initially diagnosed as idiopathic hypereosinophilia. He was finally diagnosed as hyperimmunoglobulin E syndrome with the development of cutaneous and visceral botryomycosis under steroid treatment.

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