B S. BİLGİN, M. YALAZ, N. KÜLTÜRSAY, METE AKISÜ

Kutis marmorata telenjiektatika konjenita tanılı olgu sunumu

Kutis marmorata telenjiektatika konjenita (KMTK) nadir görülen genellikle benign, sporadik, lokalize veya generalize olabilen vasküler lezyondur. Bu lezyona % 18,8 - 70 arasında anormal bulgular eşlik etmektedir. Tanı klinik bulgularla konulur ve prognozu iyidir. Bu makalede yenidoğan döneminde alt ekstremitede lokalize, asimetrik görünüm, atrofi, nadir görülen bir bulgu olan ülserasyonun eşlik ettiği bir olgu sunulmuştur. Üç aylık izleminde bulgularda düzelme gözlenmiştir.

Cutis marmorata telangiectatica congenita: A case report

Cutis marmorata telangiectatica congenita (CMTC) is a rare, usually benign, sporadic, localized or generalized vascular lesion. Abnormal findings may be associated with approximately 18.8–70% of the disease. Diagnosis of the disease is made clinically and prognosis is good. In this report, a case of CMTC with findings of asymmetrical appearence, atrophy of lower extremities accompanied by an uncommon finding of ulceration was seen in neonatal period. All these findings regressed during the 3 month follow up.

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