Abdurrahim DUSAK, Mehmet Sedat DURMAZ, Aslan BİLİCİ, Bircan ALAN

PELVİK VE BİLATERAL SİMETRİK ALT EKSTREMİTE TUTULUMLU YAYGIN FETAL KİSTİK LENFANJİOMA: OLGU SUNUMU

Yaygın fetal kistik lenfanjioma lenfatik sistemin nadir bir konjenital malfarmasyonudur.Lenfanjiomanın prognozu; lezyonun boyutu, lokalizasyonu ve birlikte olduğu diğer anomalilerinvarlığına bağlıdır. Olgumuzda maternal yaş 35, fetal BPD 27 hafta idi. Sunduğumuz bilateralproksimal ve distal alt ekstremitede ve pelvik bölgedeki yaygın fetal kistik lenfanjiomaolgusunda, pelvik bölgeden başlayıp, her iki alt ekstremiteden distale kadar devam eden cilt altıyüzeyel ve derin yumuşak dokuda çok sayıda, farklı boyutlarda yaygın keskin sınırlı ince duvarlımultiloküler kistik lezyonlar izlenmiştir. Literatür araştırmalarımızda, her iki alt ekstremiteyitutan sunulmuş bir lenfanjioma olgusuna rastlanmamıştır

Anahtar Kelimeler:

Fetüs, Lenfanjiyoma, Ultrasonografi

Pelvic And Bilateral Symetric Lower Extremities Involvement Of Extensive Fetal Cystic Lymphangioma: A Case Report

Extensive fetal cystic lymphangioma is a rare congenital malformation of the lymphatic system.Their prognosis depends on the size and location of the lesions as well as other accompanyinganomalies. Our case was 35 years, fetal BPD was 27 weeks . Herein, we present a case ofextensive fetal cystic lymphangioma that began at the pelvic area and symmetrically spannedthe bilateral proximal and distal lower extremities. Numerous extensive and sharplycircumscribed, thin walled multilobular cystic lesions in different sizes were observed in thesubcutaneous superficial and deep soft tissue beginning from the pelvic area and extending toboth lower extremities to the distal in the fetüs. To our knowledge, a case involving bothextremities has not yet been reported in the literature

Keywords:

Fetus, Lymphangioma, Ultrasonography,

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