Heval Selman ÖZKAN, Saime İRKÖREN, Hüray KARACA, Canten TATAROĞLU

Yüzde Gelişen Malign Periferik Sinir Kılıfı Tümörü Olgusu

Malign periferik sinir kılıfı tümörleri, iğsi hücreli agresif tümörer olup, yumuşak doku sarkomlarının %10’luk kısmını oluştururlar. Yüz tutulumu nadir olup, tümörler sıklıkla ekstremite ve gövdede görülür. 75 yaşında erkek hasta sol yanak bölgesinde hızlı büyüyen kitle şikayeti ile kliniğimize başvurdu. Malign periferik sinir kılıfı tümörü tanısı konan hastaya geniş eksizyon ve serbest radial ön kol flebi ile rekonstrüksiyon uygulandı. İleri yaş hastalarda baş boyun kitlelerinin ayırıcı tanısında malign periferik sinir kılıfı tümörleri düşünülmelidir.

Anahtar Kelimeler:

Malign periferik sinir kılıfı tümörü, baş boyun kitleleri, serbest flep

Malignant Peripheral Nerve Sheath Tumour With Facial Involvement

Malignant peripheral nerve sheath tumours are agressive, spindle cell sarcomas which constitute 10% of all soft tissue sarcomas. Head and neck involment is rare compared with extremity and axial involvement. 75 years old male patients referred to our clinic with a fast growing mass located in the left malar region. Malignant peripheral nerve sheath tumour diagnosis was established and wide excision and reconstruction with free radial forearm flap was performed. In elderly patients with head and neck masses malignant peripheral nerve sheath tumours must be kept in mind in differantial diagnosis.

Keywords:

Malignant peripheral nerve sheath tumour, head and neck masses, free flap,

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