Tülay DEMİRCAN, Özgür KIZILCA, MUSTAFA KIR, Baran UĞURLU, NURETTİN ÜNAL

Progresif Seyreden Kardiyak Fibromalı Bir Olgu

Çocukluk döneminde kalp tümörleri oldukça nadir görülür. Bu tümörlerin yaklaşık %90'ı iyi huyludur ve en sık görülen primer iyi huylu tümörler rabdomiyomlardır. Fibroma, miksoma ve teratama ise daha nadir görülen primer iyi huylu tümörlerdir. Bu yazıda yenidoğan döneminde yapılan ekokardiyografisinde kardiyak kitle saptanan bir olgu sunuldu. Kardiyak kitle 7 aylık izlem süresince belirgin olarak büyüdü. Hızlı ilerleme göstermesi ve sol ventrikül çıkım yoluna doğru uzanması nedeni kitle total olarak çıkartıldı. Dev kardiyak kitleye cerrahi sonrası fibroma tanısı konuldu. Kardiyak kitleler ventrikül giriş ve çıkış yolu darlığı, ritim bozukluğu ve hemodinamik bozukluk oluşturduğu zaman çıkartılmaları gerekmektedir.

Anahtar Kelimeler:

kardiyak fibroma, cerrahi, yenidoğan, dev kitle, sol ventrikül

A Case With Rapidly Progressive Cardiac Fibroma

Cardiac tumours are rarely seen in childhood. Approximately 90% of these tumors are benign and the most common benign tumor is rhabdomyoma. Fibroma, teratoma and mixoma are the other causes of benign cardiac masses. In this case we presented a newborn in whom a cardiac mass was detected in echocardiographic examination. This cardiac mass grew significantly during the postnatal 7 months. Due to rapid progression and left ventricular outflow obstruction, the mass was excised. Histopathological examination confirmed the diagnosis of fibroma. Briefly, giant masses which cause permanent rhythm abnormalities, myocardial dysfunction and ventricular inflow or outflow obstruction should be removed surgically.

Keywords:

cardiac fibroma, surgery, newborn, giant mass, left ventricul,

PDF

___

Referans1 Gerald RM, Adrian MM. Cardiac Tumors. İn:Allen HD, Driscoll DJ, Shaddy RE, Feltes T eds. Moss and Adams' Heart disease in Infants, Children, and Adolescents: Including the Fetus and Young Adult. 8.ed. Philadelphia: Lippincott Williams & Wilkins; 2013 Chapter 72.p.1549-1564.
Referans2 Uzun O, Wilson DG, Vujanic GM, Parsons JM, Giovanni J . Cardiac tumours in children. Orphanet Journal of Rare Diseases. 2007;2:11.
Referans3 Padolino MA, Vida VL, Boccuzzo G, Tonello M, Sarris GE, Berggren H et al. Surgery for Primary Cardiac Tumors in Children Early and Late Results in a Multicenter European Congenital Heart Surgeons Association Study Circulation. 2012;126:22-30.
Referans4 Yadava OP. Cardiac tumours in infancy. Indian Heart Journal. 2012;64:492-496.
Referans5 Kır M, Çatalyürek H, Karadaş U, Ünal N, Saylam G. A prenatally diagnosed newborn with an intracardiac rhabdomyoma obstructing the left ventricular outflow tract. Türk Göğüs Kalp Damar Cerrahisi Dergisi 2011;19(4):623-626.
Referans6 Kobayashi D, L’Ecuyer T, Aggarwal S. Orthotopic Heart Transplant: A Therapeutic Option for Unresectable Cardiac Fibroma in Infants. Congenit Heart Dis. 2012;7:31–36.