Mehtat ÜNLÜ, Mücahit ÖZBİLGİN, Selman SÖKMEN, Sülen SARIOĞLU

Seromüköz bez yapıları içeren bir tailgut kisti: Olgu sunumu

Retrorektal bölgede izlenen gelişimsel kistler tür, köken ve histopatolojik özelliklerine göre epidermoid kist, rektal duplikasyon (enterik) kisti ve retrorektal kistik hamartoma (“tailgut kisti”) olarak sınıflandırılabilir. Bu kistler benign gelişimsel lezyonlar olmakla birlikte, nadir de olsa malign dönüşüm bildirilmektedir. Bu nedenle klinik olarak erken tanı çok önemlidir. Nadir görülen bu lezyonlar patolog için de ayırıcı tanı açısından sıkıntı yaratabilir. Embriyolojik hindgut kalıntılarından gelişen tailgut kistleri genellikle multikistik olup, skuamöz epitel, silli kolumnar epitel ya da transisyonel epitel ile döşelidir. Literatürde kist duvarında organize bez yapısı tanımlanan olgu bulunmamaktadır. Burada, altmış sekiz yaşında retrorektal kitlesi bulunan ve histopatolojik tanısı tailgut kisti ile uyumlu, kist duvarında serömüköz bezler bulunan bir olgu sunulmuş ve retrorektal gelişimsel kistlerin ayırıcı tanısı tartışılmıştır.

Taılgut cyst wıth seromucous glandular structures: Case report

Developmental cysts in the retrorectal region can be classified as epidermoid, rectal duplication (enteric) cyst and cystic hamartoma ("tailgut cyst"), according to the origin and histopathologic features. These cysts are benign developmental lesions, although malignant transformation has been rarely reported. Therefore, early diagnosis is important. Because they are rare, differential diagnosis of these lesions may cause trouble for the pathologist. Tailgut cyst develops from embriologic hindgut and usually occurs as a multiloculated cyst lined by squamous, transitional, or glandular epithelium. Here in, we present a sixty-eight year old man with organized glandular structures of the cyst wall. To the best of our knowledge, this is the first reported tailgut cyst, with organized glandular structures, seromocous glands.

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