Fahr Sendromu Olan Hastada Anestezi Yönetimi: Olgu Sunumu

Fahr sendromu, serebellum, bazal gangliyonlar gibi alanlarda simetrik intrakraniyal kalsifikasyonlarla karakterize nörodejeneratif bir hastalıktır. Kalsiyum ve fosfor metabolizmasının bozuk olduğu bu hastalıkta hipokalseminin tespit ve tedavisi anestezi uygulaması açısından önem taşımaktadır. Olgu sunumunda 64 yaşında hipoparatiroidi ile ilişkili Fahr Sendromu tanısı olan hastanın genel anestezi yönetimi irdelenmiştir.

Anahtar Kelimeler:

Fahr Sendromu, bazal ganglia hastalıkları anestezi, hipokalsemi, hipoparatiroidizm

ANESTHESIA MANAGEMENT IN PATIENT WITH FAHR’S SYNDROME: A CASE REPORT

Fahr’s syndrome is a neurodegenerative disease characterized by symmetric intracranial calcifications in areas such as the cerebellum and basal ganglia. Detection and treatment of hypocalcemia in this disorder, where calcium and phosphorus metabolism is impaired, is important for anesthesia application. This article describes the general anesthesia management of a 64-year-old patient with Fahr’s syndrome associated with hypoparathyroidism.

Keywords:

Fahr’s syndrome basal ganglis diseases, anesthesia, hypocalcemia, hypoparathyroidism,

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