Salih BAKIR, İsmail YILDIZ, Yahya SAĞLIKER

Sağlıker sendromlu hastalarda işitme fonksiyonunun değerlendirilmesi

Amaç: Bu çalışmanın amacı Sağlıker sendromlu hastalardaki işitme fonksiyonlarını değerlendirmektir. Sağlıker sendromu literatüre 2000 yılında girmiş olan ve görülme sıklığı KBY hastalarında % 0.5 olarak bildirilen, geri kalmış ülkelerde sık görülen yeni bir sendromdur. Sendroma neden olan faktörler henüz kesin olarak bilinmemekte ve bu konuda halen çalışmalar devam etmektedir. Bu sendromda kronik böbrek hastalığı ve bunun yetersiz tedavisine bağlı sekonder hiperparatiroidizm yanında, kafada şekil bozuklukları, kısa boy, maksiller ve mandibuler kemikte değişiklikler, diş anomalileri, ağız boşluğu içerisinde yumuşak doku tümörleri, parmak uçlarında değişiklik gibi her türlü kemik anomalisi gelişebilir. Bu bulgulara psikolojik sorun- lar, depresyon ve işitme kaybı eşlik edebilir. Gereç ve Yöntem: Bu çalışmada, sağlıker sendromu nedeniyle takip edilen ve hemodiyaliz tedavisi almakta olan 12 hastada otoskopik muayene, Weber ve Rinne testleri, saf ses odyometrisi ve timpanometri test sonuçları sunuldu. Bulgular: Olguların 5 tanesinde (% 41.7) sensörinöral tipte işitme kaybı saptandı. Bu sonuç Sağlıker sendromunda işitme kaybı olasılığının hayli yüksek olduğunu düşündürmektedir Sonuç: Hastalarımızın tümünün hemodiyaliz tedavisi almakta oluşu nedeniyle hemodiyaliz işitme kaybına yol açabilecek bir etken olarak düşünülebilir.

Evaluation of hearing function in patients with Sağlıker Syndrome

Aim: The aim of this study was to evaluate th hearing functions of patients with Sagliker syndrome. Sagliker syndrome is a new disease entity that firstly has been described at year 2000. The frequency of this syndrome has been reported as approximately 0.5% of patient with chronic renal failure and mostly seen in poor and underdeveloped countries. The definite causes of this entity has not been not been clearly understood yet, however studies on risk factors that can lead to this syndrome are underway. Sagliker Syndrome seems to be related to chronic kidney disease and secondary hyperparathyroidism. Every kind of bone abnormalities including, skull deformities, short stat- ure, maxillary and mandibulary changes, teeth abnormalities, soft and harmless tumoral tissues in the mouth and fingertip changes can develop. Psychological problems and depression may accompany these findings Materials and Methods: In present study, 12 patients with Sagliker Syndrome were retrospectively evaluated. Audiological tests were performed on these patients, including otoscopic examinations, Rinne and Weber tests, pure tone odiometry and timpanometry. Results: Five patients (41.7%) were found to have sensorineural type hearing loss. According to our results with a limited number of patients, hearing loss potential seems to be high with Sagliker Syndrome. Conclusion: Haemodialysis can be suggested as a risk factor on hearing loss of Sagliker syndrome, since all of our patients were on hemodialysis.

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